Glossary -   Pulmonary atresia (with intact septum)

 

 

Pulmonary atresia (with intact septum) is a heart defect present at birth with two main differences from a normal heart:

  • The valve which allows blood to flow from the heart to the lungs – the pulmonary valve – is completely blocked, and
  • The main pumping chamber on the right side – the right ventricle – has not developed normally.